[Pityriasis lichenoides et varioliformis acuta (Mucha-Habermann disease)].

Pityriasis Lichenoides Et Varioliformis Acuta (Mucha-Habermann Disease)

Febrile ulceronecrotic Mucha-Habermann disease: a case report and review of the literature.

A 32-year-old male with febrile ulceronecrotic Mucha-Habermann disease (FUMHD) responsive to methotrexate is reported. This is a severe variant of pityriasis lichenoides et varioliformis acuta characterized by the acute onset of a widespread ulceronecrotic cutaneous eruption together with high fever and systemic involvement. To our knowledge, only 13 patients with FUMHD have been reported to date.

Methotrexate Treatment in Children with Febrile Ulceronecrotic Mucha-Habermann Disease: Case Report and Literature Review

Febrile Ulceronecrotic Mucha-Habermann disease is a rare and potentially fatal variant of pityriasis lichenoides et varioliformis acuta and is characterized by high fever, constitutional symptoms, and acute oncet of ulceronecrotic lesions. We present an 11-year-old male with Febrile Ulceronecrotic Mucha-Habermann disease who was cured with methotrexate and review the use of methotrexate for thi...

Pityriasis lichenoides chronica presenting with bilateral palmoplantar involvement.

Pityriasis lichenoides is an uncommon, acquired, idiopathic, self-limiting skin disease that poses a challenge to patients and clinicians to diagnose and treat. Several variants exist including pityriasis lichenoides et varioliformis acuta (PLEVA), pityriasis lichenoides chronica (PLC), and febrile ulcer-onecrotic Mucha-Habermann disease. Precise classification can be difficult due to an overla...

A fatal case of febrile ulceronecrotic Mucha-Habermann disease in a child

ABS: antibiotics DDS: diamino-diphenyl sulphone FUMHD: Febrile ulceronecrotic MuchaHabermann disease IVIG: intravenous immunoglobulins MI: mucosal involvement MTX: methotrexate PLEVA: pityriasis lichenoides et varioliformis acuta SI: systemic involvement SS: systemic steroids INTRODUCTION Febrile ulceronecrotic Mucha-Habermann disease (FUMHD) is a rare, potentially fatal, severe variant of pity...

Febrile ulceronecrotic Mucha–Habermann disease: a case report and a review of the literature

This report describes the case of a 76 year old man who suffered from febrile ulceronecrotic Mucha–Habermann disease (FUMHD). Despite this patient’s typical clinical and histological findings, the fulminating course led to death. Polymerase chain reaction (PCR) analysis of the skin lesions showed that the infiltrating cells were monoclonal in origin and were from an aberrant clone. FUMHD is a v...